Mitochondrial intermembrane space
- CPOX: coproporphyrinogen oxidase
- GATM: glycine amidinotransferase (L-arginine:glycine amidinotransferase)
- HSD3B2: hydroxy-delta-5-steroid dehydrogenase, 3 beta- and steroid delta-isomerase 2
- OPA1: optic atrophy 1 (autosomal dominant)
- PANK2: pantothenate kinase 2
- PPOX: protoporphyrinogen oxidase
- TIMM8A: translocase of inner mitochondrial membrane 8 homolog A (yeast)
Source: Gene Ontology Consortium
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