Mitochondrial membrane part
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External side of mitochondrial outer membrane
- LRRK2: leucine-rich repeat kinase 2
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Integral to mitochondrial membrane
- CPT1A: carnitine palmitoyltransferase 1A (liver)
- DMPK: dystrophia myotonica-protein kinase
- ETFDH: electron-transferring-flavoprotein dehydrogenase
- GDAP1: ganglioside induced differentiation associated protein 1
- L2HGDH: L-2-hydroxyglutarate dehydrogenase
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Intrinsic to mitochondrial inner membrane
- ETFDH: electron-transferring-flavoprotein dehydrogenase
- L2HGDH: L-2-hydroxyglutarate dehydrogenase
- PPOX: protoporphyrinogen oxidase
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Intrinsic to mitochondrial outer membrane
- CPT1A: carnitine palmitoyltransferase 1A (liver)
- DMPK: dystrophia myotonica-protein kinase
- GDAP1: ganglioside induced differentiation associated protein 1
- MFN2: mitofusin 2
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Mitochondrial crista
- OPA1: optic atrophy 1 (autosomal dominant)
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Mitochondrial proton-transporting ATP synthase complex
- MT-ATP6: mitochondrially encoded ATP synthase 6
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Mitochondrial proton-transporting ATP synthase complex, coupling factor F(o)
- MT-ATP6: mitochondrially encoded ATP synthase 6
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Mitochondrial respiratory chain
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Mitochondrial respiratory chain complex I
- MT-ND1: mitochondrially encoded NADH dehydrogenase 1
- MT-ND4: mitochondrially encoded NADH dehydrogenase 4
- MT-ND4L: mitochondrially encoded NADH dehydrogenase 4L
- MT-ND5: mitochondrially encoded NADH dehydrogenase 5
- MT-ND6: mitochondrially encoded NADH dehydrogenase 6
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Mitochondrial respiratory chain complex II
- SDHA: succinate dehydrogenase complex, subunit A, flavoprotein (Fp)
- SDHB: succinate dehydrogenase complex, subunit B, iron sulfur (Ip)
- SDHC: succinate dehydrogenase complex, subunit C, integral membrane protein, 15kDa
- SDHD: succinate dehydrogenase complex, subunit D, integral membrane protein
Source: Gene Ontology Consortium
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